Secretory Leukocyte Protease Inhibitor Protein Regulates the Penetrance of Frontotemporal Lobar Degeneration in Progranulin Mutation Carriers Manuscript Number: 13-1163R1 Author(s): Luisa Benussi, Giuliano Binetti, Loredana Caruana, Rosa Flocco, Roberta Ghidoni, Michela Glionna, Anna Paterlini, Elisa Tonoli